肾和肝组织的宏观和微观特征。肾脏(a e): (a)严重扩散垂直多囊肾实质的改变。皮质和髓质失败的歧视。正常大小的双肾规模(左上角)。(b, c)多囊肾实质的改变(星号)是由扁平上皮衬里。多病灶的息肉状遍布/预测的管状上皮(细箭头)。此外,有单一形态成熟肾小球(箭头)。间质组织的特征是一个微妙的维管组织的基质,血管,和众多的萎缩性/坏死小管(粗箭头)。苏木精和伊红(他)(d)状遍布/预测(箭头所指)由凸圆卵形的细胞,偶尔发生泡沫/析稀淡嗜酸性胞浆。他(e)纤维突出道路两旁isoprismatic上皮是显而易见的。 HE. Liver: (f) multifocal proliferated and dilated biliary ducts (asterisk), surrounded by marked pericholangiolar bridging fibrosis (green). Occasionally, supraepithelial granular structures can be seen (arrow). Numerous blood vessels occur with a marked perivascular fibrosis (inset). Masson’s Trichrome.