机构组织,TY -的A2 Ferreri Florinda盟——Mastrolilli f . AU - Benvenga, a . AU - Di Biase l . AU - Giambattistelli f . AU - Trotta l . AU - Salomone g . AU - Quintiliani l . AU -蓝迪,d . AU - Melgari j . m . AU - Vernieri f . PY - 2011 DA - 2011/07/12 TI -一个不寻常的痴呆的原因:基本诊断的元素Corticobasal Degeneration-A病例报告和文献回顾SP - 536141六世- 2011 AB - Corticobasal变性(CBD)是一种罕见的,零星的,神经退行性疾病的中期late-adult生活。我们描述一个进一步的病理异质性条件的例子。一个71岁的女人最初出现构音障碍、笨拙、进步不对称动作迟缓,左臂和刚度。刚度逐渐涉及到同侧腿;姿势不稳定与瀑布、睑痉挛和吞咽困难随后发达。之前她已经诊断为帕金森病反应迟钝。在我们的临床检查,她提出离开upper-arm-fixed-dystonia,左下肢痉挛状态和锥体(巴宾斯基和霍夫曼)迹象。脑部核磁共振成像显示不对称右额颞叶皮层的大脑皮层萎缩。神经心理学检查显示在视觉空间的功能障碍,frontal-executive障碍,hemineglect。这个案例表明,协会不对称焦皮层和皮层下功能仍然是这种情况的临床特点。 There are no absolute markers for the clinical diagnosis that is complicated by the variability of presentation involving also cognitive symptoms that are reviewed in the paper. Despite the difficulty of diagnosing CBD, somatosensory evoked potentials, motor evoked potentials, long latency reflexes, and correlations between results on electroencephalography (EEG) and electromyography (EMG) provide further support for a CBD diagnosis. These techniques are also used to identify neurophysiological correlates of the neurological signs of the disease. SN - 2090-8024 UR - https://doi.org/10.4061/2011/536141 DO - 10.4061/2011/536141 JF - International Journal of Alzheimer’s Disease PB - SAGE-Hindawi Access to Research KW - ER -