TY -的A2时,阿里f . AU - Electricwala,阿里•j . AU - Electricwala于jaf t . PY - 2016 DA - 2016/11/08 TI -主要脊椎尤文氏肉瘤的一个两岁的男孩SP - 8027137六世- 2016 AB -尤文氏肉瘤(ES)是一种高度恶性骨肿瘤。它可能涉及骨骼的任何部位，但最常见的部位是髂骨、股骨骨干和胫骨(Alfeeli et al.， 2005;朱等，2012)。脊柱原发性ES极其罕见(Yan等人，2011年)。它只占所有原发性骨肉瘤的3.5% - 14.9%。发病年龄从12岁到24岁(中位数21岁)(Ferguson, 1999;Sharafuddin等人，1992年;Klimo Jr.等人，2009)。我们报告一个不寻常的病例原发性脊柱ES在一个两岁的男孩，谁向我们提出麻痹和特征的马尾综合征。核磁共振扫描显示肿瘤肿块起源于L4椎弓根侵犯椎管。 Tc-99 bone scan showed increased tracer uptake in L4 vertebra and normal tracer uptake elsewhere in the skeleton. After reaching the diagnosis of a space occupying lesion invading the lumber spinal canal, we performed a decompressive laminectomy and a biopsy was sent which confirmed the diagnosis of ES. Immunohistochemistry showed tumour cells staining positive for CD-99 (specific stain for ES). Gene testing showed an EWS-FLI 1 chimera. Surgery was followed by good improvement in motor signs. The child was then referred to a specialized oncotherapy centre for further treatment, radiation, and chemotherapy. To the best of our knowledge, we are the first to report primary ES of the spine at the age of two years. SN - 2090-6749 UR - https://doi.org/10.1155/2016/8027137 DO - 10.1155/2016/8027137 JF - Case Reports in Orthopedics PB - Hindawi Publishing Corporation KW - ER -