TY -的A2 Varela-Centelles巴勃罗。非盟- Koruyucu,我非盟- Barlak Pelin盟——Seymen Figen PY - 2014 DA - 2014/12/24 TI -口头和牙科角化不良的结果Congenita SP - 454128六世- 2014 AB -先天性角化不良(DC)是一种罕见的疾病,其特征是网状皮肤色素沉着过度,粘膜白斑、甲营养不良。更严重的特点是骨髓参与全血细胞减少症和恶性肿瘤的易感性。本病例报告的目的是描述直流综合症患儿的口腔和牙科的发现。一个10岁的男性被诊断为直流承认是因为广泛的龋齿和牙痛。口腔卫生和广泛的观察龋齿不足病人的口试。菌斑堆积在上颌牙齿的牙龈边境。舌乳头萎缩是观察。短而迟钝的根下颌骨门齿和上、下磨牙测定射线探伤。干燥的嘴唇和commisuras,外翻的眼睛,和泪被观察到。进行血液测试,表明再生障碍性贫血2岁。 At the age of 4, the bone marrow transplantation was performed. Dermatological findings occurred after the bone marrow transplantation. The skin of the patient was thin, dry, and wrinkled in some areas. He had palmoplantar hyperkeratosis and syndactylia on his fingers. Endodontic treatment procedures were applied and other extensive caries are still being restored. The patient will be given full preventive care during regular follow-up. Oral hygiene was improved to the optimum level. SN - 2090-6447 UR - https://doi.org/10.1155/2014/454128 DO - 10.1155/2014/454128 JF - Case Reports in Dentistry PB - Hindawi Publishing Corporation KW - ER -